Orbit sarcoma
Contents:
Description:
Sarcoma of an orbit belongs to primary malignant tumors of a connective tissue origin.
Orbit sarcoma reasons:
The etiology is unknown. Histologically distinguish the following main types of sarcomas: kruglokletochny, polimofnokletochny, fusocellular and fibrosarcoma. The majority of sarcomas of an orbit — especially malignant tumors. They differ in the rapid infiltrative growth, bent to a recurrence and early metastasises. Development of process depends on primary localization of a tumor in an orbit and growth rate of a tumor.
Orbit sarcoma symptoms:
Develops preferential at the age of 6 — 11 years. Process, as a rule, unilateral. Primary growth of a tumor is more often observed in an upper part of an eye-socket. Are noted a hyperemia and the century swelled. Arises хемоз conjunctivas, the ptosis appears. It usually is followed by feeling of a raspiraniye in an orbit and pain behind an eye. Eyeglobe shift, restriction of its mobility is noted. The leading symptom — emergence and bystry progressing of a unilateral exophthalmos which sometimes reaches 25 — 30 mm. Early there come visual frustration and changes on an eyeground: a congestive optic disk, its atrophy, hemorrhages and the degenerative centers in a retina. At a big exophthalmos there are trophic disturbances in a cornea in the form of decrease in its sensitivity, emergence of erosion and ulcers. The tumor can burgeon in paranasal sinuses or in a head cavity. Radiological are defined blackout in an eye-socket, at slower development of a tumor — increase in an eye-socket, destructive changes in bone walls.
Orbit sarcoma
Diagnosis:
The diagnosis is made on the basis of clinical signs and X-ray inspection. Recognition is helped an ultrasonic and radio isotope research. At differential diagnosis it must be kept in mind an endocrine exophthalmos, vascular tumors of an orbit, inflammatory diseases of an eye-socket and other tumors of an orbit.
Treatment of sarcoma of an orbit:
Are shown an early ekzenteration of an orbit with the subsequent radiation therapy and chemotherapy.
The forecast is adverse.
